Dr Ahmed Sherif
Aswan Heart Center, Egypt
Biography
Ahmed Masoud has completed his MRCPCH and is currently a member of the Royal College of Paediatrics and Child Health, UK. He is currently a senior Paediatric CICU registrar at Aswan Heart Centre, Aswan, Egypt.
Ahmed Sherif has completed his MSc. in Paediatrics and Neonatology degree from Ain Shams University, Egypt. He has also completed the MRCPCH exams and is currently a member of the Royal College of Paediatrics and Child Health, UK. He has been working at Aswan Heart Centre, Aswan, Egypt, but currently he is a senior PICU Clinical Fellow at Great Ormond Street Hospital, London, UK
Abstract
A 2 month old boy who presented with complete heart block and had a permanent pace maker inserted surgically at the age of 6 weeks was readmitted with mediastinitis and wound infection. His mother was diagnosed with systemic lupus erythematosis and he had a positive lab test for both anti Ro and anti La antibodies. He was noticed to be leucopenic and with further investigation, he was found to have severe combined immune deficiency (SCID) which was rarely reported to be associated with maternal systemic lupus and was more rare to present with congenital complete heart block.